Immunophenotyping lymphocyte and acute phase proteins in canine X-linked muscular dystrophy
نویسندگان
چکیده
منابع مشابه
X linked muscular dystrophy with contractures.
Another family with X linked muscular dystrophy affecting particularly the humeral and tibial muscles is described. Cardiomyopathy in the eldest male necessitated the insertion of a pacemaker.
متن کاملReduction of the transient outward potassium current in canine X-linked muscular dystrophy.
BACKGROUND The xmd dog develops a cardiomyopathy similar to that seen in Duchenne muscular dystrophy patients. In both the canine and human diseases, ECG abnormalities may precede the development of overt cardiac pathological lesions. The purpose of this study was to determine whether specific cellular electrical abnormalities occur in dystrophic ventricular tissue. METHODS AND RESULTS Action...
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This report describes a family showing muscular dystrophy and atrioventricular block with an x-linked hereditary transmission. Among a known pedigree of 101 family members, 12 males were found to have skeletal muscle involvement and six needed pacemakers around age 30 years. Unlike the x-linked muscular dystrophies of Duchenne and of Becker, the predominant skeletal involvement was in humeral m...
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ژورنال
عنوان ژورنال: Anais da Academia Brasileira de Ciências
سال: 2018
ISSN: 1678-2690,0001-3765
DOI: 10.1590/0001-3765201820170838